Definition of Acylcarnitines. Meaning of Acylcarnitines. Synonyms of Acylcarnitines

- transiently attached to the hydroxyl group of carnitine to form fatty acylcarnitine. This transesterification is catalyzed by an enzyme found in the outer...
- The enzyme acylcarnitine hydrolase (EC 3.1.1.28) catalyzes the reaction O-acylcarnitine + H2O ⇌ {\displaystyle \rightleftharpoons } a fatty acid + L-carnitine...
- Carnitine-acylcarnitine translocase (CACT) is responsible for p****ive transport of carnitine and carnitine-fatty acid complexes and across the inner mitochondrial...
- Carnitine-acylcarnitine translocase deficiency is a rare, autosomal recessive metabolic disorder that prevents the body from converting long-chain fatty...
- palmitoyltransferase II) and transported back outside so the process can occur again. Acylcarnitines like palmitoylcarnitine are produced as intermediate products of the...
- after birth, by the analysis of blood spots collected on filter paper. Acylcarnitine profiles with MS/MS will show a very characteristic pattern of elevated...
- cardioprotection aspect of Intralipid is initiated by the ac****ulation of acylcarnitines in the mitochondria and involves inhibition of the electron transport...
- membrane (and hence effectively out of the mitochondria) via carnitine-acylcarnitine translocase (39). 3HIA-carnitine is thought to be either directly deacylated...
- of orotic acid, as well as rule out an organic acidemia) and plasma acylcarnitines (will be normal in OTC deficiency, but can identify some other causes...
- converts acyl-CoA into acylcarnitine, which gets transported into the mitochondrial matrix.  Once in the matrix, acylcarnitine is converted back to acyl-CoA...