-
Carnitine is a
quaternary ammonium compound involved in
metabolism in most mammals, plants, and some bacteria. In
support of
energy metabolism, carnitine...
- Acetyl-L-
carnitine,
ALCAR or ALC, is an
acetylated form of L-
carnitine. It is
naturally produced by the
human body, and it is
available as a
dietary supplement...
-
Carnitine palmitoyltransferase I (CPT1) also
known as
carnitine acyltransferase I, CPTI, CAT1, CoA:
carnitine acyl
transferase (CCAT), or
palmitoylCoA transferase...
-
Carnitine palmitoyltransferase II deficiency,
sometimes shortened to CPT-II or CPT2, is an
autosomal recessively inherited genetic metabolic disorder...
-
Carnitine O-acetyltransferase also
called carnitine acetyltransferase (CRAT, or CAT) (EC 2.3.1.7) is an
enzyme that
encoded by the CRAT gene that catalyzes...
-
primary carnitine deficiency (SPCD) is an
inborn error of
fatty acid
transport caused by a
defect in the
transporter responsible for
moving carnitine across...
-
Carnitine O-palmitoyltransferase (also
called carnitine palmitoyltransferase) is a
mitochondrial transferase enzyme (EC 2.3.1.21)
involved in the metabolism...
-
Carnitine O-palmitoyltransferase 2,
mitochondrial is an
enzyme that in
humans is
encoded by the CPT2 gene.
Carnitine palmitoyltransferase II precursor...
-
carnitine O-octanoyltransferase is an
enzyme that in
humans is
encoded by the CROT gene.
Carnitine octanoyltransferase (EC 2.3.1.137) is a
carnitine acyltransferase...
-
Carnitine palmitoyltransferase I
deficiency is a rare
metabolic disorder that
prevents the body from
converting certain fats
called long-chain
fatty acids(LCFA)...