Definition of Acylcarnitine. Meaning of Acylcarnitine. Synonyms of Acylcarnitine

- transiently attached to the hydroxyl group of carnitine to form fatty acylcarnitine. This transesterification is catalyzed by an enzyme found in the outer...
- The enzyme acylcarnitine hydrolase (EC 3.1.1.28) catalyzes the reaction O-acylcarnitine + H2O ⇌{\displaystyle \rightleftharpoons } a fatty acid + L-carnitine...
- Carnitine-acylcarnitine translocase deficiency is a rare, autosomal recessive metabolic disorder that prevents the body from converting long-chain fatty...
- Carnitine-acylcarnitine translocase (CACT) is responsible for p****ive transport of carnitine and carnitine-fatty acid complexes and across the inner mitochondrial...
- after birth, by the analysis of blood spots collected on filter paper. Acylcarnitine profiles with MS/MS will show a very characteristic pattern of elevated...
- inner mitochondrial membrane via a transporter protein called carnitine-acylcarnitine translocase. Once inside, carnitine is liberated (catalysed by the enzyme...
- Hach may refer to: Acylcarnitine hydrolase, enzyme that catalyses the hydrolysis of acylcarnitine Hach (surname), or people with that surname Hach Company...
- membrane (and hence effectively out of the mitochondria) via carnitine-acylcarnitine translocase (39). 3HIA-carnitine is thought to be either directly deacylated...
- - SLC22A5 (carnitine transporter) Carnitine-acylcarnitine translocase deficiency - Carnitine-acylcarnitine translocase Carnitine palmitoyltransferase I...
- converts acyl-CoA into acylcarnitine, which gets transported into the mitochondrial matrix.  Once in the matrix, acylcarnitine is converted back to acyl-CoA...